Primary involvement of kidney is rare in cases of hydatid disease. The causative agent is Echinococcus granulosus, a dog tape worm. Human functions as a dead end intermediate host. Liver and Lungs are the most common sites of involvement in case of echinococcosis. We present a case of primary left renal hydatid cyst in a 40 year old female patient admitted with left lumbar pain radiating to back and dysuria. Ultrasonography revealed it as a multiloculated cystic mass and left nephroureterectomy was done after a provisional diagnosis of renal hydatid cyst was done. Multiple translucent daughter cysts were found preoperatively a final diagnosis of primary hydatid cyst of kidney was made after histopathological examination. Open surgery is the treatment of choice with an excellent result and the patient is doing well postoperatively.