Pleomorphic adenoma is the most common salivary gland tumour, which accounts for 60-65% of such cases. It usually involves major salivary glands. However it also involves minor salivary glands of oral cavity and oropharynx. In oral cavity, hard palate is the most common site. Other rare sites are lips, buccal mucosa, alveolar ridge, floor of the mouth and tongue. This case report describes a rare and unusual presentation of pleomorphic adenoma in upper lip.